|
||||||||
![]() |
||||||||
Types:
|
Type ΙThis is the most common and mildest type in which the common features are the following: • Bones are predisposed to fracture, with most fractures occurring before puberty with the number of fractures not being bigger than 20 – 40 fractures. • Stature is normal or near – normal. • Joints are loose and muscle tone is low. • Usually sclera (whites of the eyes) have blue, purple or gray tint. • Face shape is triangular. • Tendency toward scoliosis (a curvature of the spine). • Bone deformity is absent or minimal • Dentinogenesis imperfecta may occur, causing brittle teeth. • Hearing loss is a possible symptom, often beginning in early 20s or 30s. • Structure of collagen is normal, but the amount is less than normal. |
Type ΙΙThis type is the most severe form of O.I. The common features of it are the following: • O.I. Type II is lethal shortly after birth, often as a result of respiratory problems. • Fractures are numerous and bone deformity is severe • Stature is small with undeveloped lungs. • Collagen is formed improperly. • In recent years people with osteogenesis imperfecta type 2 have reached their early adult years. |
Type ΙΙΙCommon symptoms are: • Bones fracture easily and people with O.I. Type III may have more than 100 fractures before puberty. Fractures are often present at birth, and x rays may reveal healed fractures that occurred before birth. • Stature is significantly shorter than normal. • Usually sclera (whites of the eyes) have blue, purple or gray tint. • Face shape is triangular. • Scoliosis (a curvature of the spine) is present.. • Joints are loose and muscle development is poor in arms and legs. • Rib cage is barrel – shaped. • Respiratory problems are possible. • Bone deformity is often severe. • Dentinogenesis imperfecta may occur, causing brittle teeth. • Hearing loss is possible |
Type ΙVThis Type falls between Type I and Type III in severity. Among the common features of it are the following: • Bones fracture easily, with most fractures occurring before puberty. • Stature is shorter than average. • Sclera (whites of the eyes) is normal in color, appearing white or near – white. • Bone deformity is mild to moderate. • Scoliosis (curvature of the spine) is likely. • Rib cage is barrel- shaped. • Face is triangular in shape. • Dentinogenesis imperfecta may occur, causing brittle teeth. • Hearing loss is possible • Collagen is formed improperly. |